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anakinra (PerkinRA)

✓ Approved

PersisGen Par · IL1R1 · Recombinant Proteins

What is anakinra?

anakinra is a recombinant proteins developed by PersisGen Par. It is approved for therapeutic indications via injectable (others) or intravenous (iv) or subcutaneous injection.

Drug Profile

Brand NamesPerkinRA
CompanyPersisGen Par
Drug ClassRecombinant Proteins
Molecular TargetIL1R1
RouteInjectable (Others), Intravenous (IV), Subcutaneous Injection
StatusApproved

Mechanism of Action

Molecular Targets

anakinra acts on 1 molecular target:

IL1R1interleukin 1 receptor type 1 (P80, CD121A)
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Therapeutic Indications

anakinra is developed for 11 unique indications across 5 therapeutic areas.

Therapeutic AreaConditionPhase
Musculoskeletal and connective tissue disordersRheumatoid arthritis✓ Approved
Musculoskeletal and connective tissue disordersStill's disease✓ Approved
Musculoskeletal and connective tissue disordersJuvenile idiopathic arthritis✓ Approved
Congenital, familial and genetic disordersChronic infantile neurological cutaneous and articular syndrome✓ Approved
Congenital, familial and genetic disordersMuckle-Wells syndrome✓ Approved

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Related Research Articles

PubMedFrontiers in immunology2026-07-25

The cell-mediated adaptive immune response to herpes simplex virus type 1 encephalitis: mechanisms and clinical implications.

Osborne Louise L, Dunai Cordelia C, Huang Yun Y, Egbe Franklyn N FN et al.

Herpes simplex virus (HSV) encephalitis is the most frequent cause of sporadic encephalitis globally. Despite the emergence of the antiviral drug aciclovir curtailing mortality, this disease remains a clinical challenge due to its rapid progression and associated neurological sequelae; indicating the urgent requirement for adjunctive neuroprotective treatment options. Recent studies using both human samples and murine models have highlighted how cell mediated immune cells including CD8+, CD4+ and brain tissue-resident memory T cells have the capacity to act as a 'double-edged sword'; both serving to protect the host against HSV encephalitis, but also increasing neuroglial injury by inflammation. Factors which impair cell-mediated immunity may predispose individuals to herpes simplex encephalitis, including defects in viral immune evasion strategies (infected cell protein 47, UL13 kinase), host genetic pre-disposition (toll-like receptor 3 deficiency, lymphotoxin-α deficiency, Rel mutations) and external factors such as stress. Additionally, there is a particular need for clinical vigilance for patients on immunosuppressive treatments which impair cell-mediated immunity, including azathioprine, hydroxychloroquine and methotrexate. Conversely, understanding these molecular mechanisms may provide new insights into the use of immunomodulatory strategies including anakinra, tocilizumab, and the implementation of targeted vaccination. This review summarises the current state of knowledge of how an impaired cell-mediated immune response could promote herpes simplex virus encephalitis, followed by an exploration of the clinical applications and therapeutic interventions which could viably be implemented to ameliorate immune-mediated tissue injury.

PubMedJournal of clinical neuroscience : official journal of the Neurosurgical Society of Australasia2026-07-25

Cerebrovascular involvement in Erdheim-Chester disease: a case report and systematic literature review.

Delacotte Claire C, Arnaud Charlotte C, de Boysson Hubert H, Aouba Achille A et al.

Intracranial perivascular/vascular infiltrations and stenoses related to Erdheim-Chester disease (ECD), often associated with ischemic events, are rarely documented. This study aims to characterize intracranial perivascular/vascular infiltrations and stenoses. We first report a new case of strokes revealing ECD with intracranial arterial involvement. We then searched all English- and French-language publications from database inception to November 2025 across 12 different search interfaces, including grey literature sources. Vascular involvement was defined by the presence of intracranial perivascular/vascular infiltrations and stenosis on imaging and/or histopathological evidence of small-vessel involvement. Cases with intracranial nodules or masses abutting vessels but without clear longitudinal perivascular infiltration were excluded. We present a case of recurrent strokes with intracranial vertebral and basilar artery wall stenosis, and aortitis. Initially diagnosed as giant cell arteritis, the patient was treated with corticosteroids, cyclophosphamide followed by methotrexate, but relapsed. The identification of tibial osteosclerosis led to the diagnosis of ECD, with a favorable response to anakinra. Twelve relevant articles were retrieved, in addition to our own case. Most patients exhibited focal cerebrovascular signs (11/13) and associated parenchymal involvement (11/13). Intracranial perivascular/vascular infiltrations and stenoses involved the carotid arteries (7/13), the vertebrobasilar arteries (1/13), or both territories (4/13). Aorta was involved in 8/12 cases. Among the nine patients with available follow-up data, five had poor overall or neurovascular outcomes. Intracranial perivascular/vascular infiltrations and stenoses, which leads to recurrent focal ischemic events, represents a likely underdiagnosed CNS pattern in ECD, referred to as "cerebrovascular ECD", which worsens overall prognosis. Vascular imaging should be included in brain MRI protocols for patients with ECD, given the overlap with parenchymal involvement.

PubMedLa Revue de medecine interne2026-07-23

Blocking interleukin-1 in pericarditis: Should we move earlier and stronger?

Michaud Martin M, Jamilloux Yvan Y

Acute pericarditis is generally a benign condition, yet 15-30% of patients will develop recurrent pericarditis. Standard first-line therapy combines non-steroidal anti-inflammatory drugs or aspirin with colchicine, which reduces but does not eliminate the risk of recurrence. Patients presenting with a high inflammatory burden, subacute evolution or large pericardial effusion are particularly prone to recurrence, and corticosteroid exposure - still frequent in clinical practice - further increases this risk. Over the last decade, the central role of interleukin-1 (IL-1) in pericardial inflammation has been demonstrated, and IL-1 inhibitors have emerged as the most effective treatment for colchicine-resistant or corticosteroid-dependent recurrent pericarditis. Anakinra, rilonacept and other IL-1-targeting agents provide rapid symptom resolution and dramatically reduce recurrences, thereby transforming the management of difficult-to-treat forms of the disease. This review summarizes current knowledge on the IL-1 pathway in pericarditis and examines whether earlier, targeted intervention could modify disease trajectory, particularly in patients identified as having a high risk of recurrence at presentation. Drawing parallels with Still's disease, in which early IL-1 inhibition improves long-term outcomes, these data support the need for high-quality trials evaluating IL-1 blockade as a first-line strategy in selected patients with acute pericarditis.

PubMedExpert opinion on biological therapy2026-07-19

Anakinra treatment practices in colchicine-resistant familial Mediterranean fever: a survey of pediatric rheumatologists conducted through the PReS AID-WP and the Turkish pediatric rheumatology associations.

Atamyıldız Uçar Sıla S, Tunce Eray E, Sözeri Betül B

Colchicine-resistant familial Mediterranean fever (cr-FMF) represents a therapeutic challenge, and anakinra, a recombinant interleukin-1 receptor antagonist, is widely used in clinical practice. Our aim was to describe real-world practices of pediatric rheumatologists regarding anakinra use in patients with cr-FMF, with a focus on treatment initiation, tapering strategies, and discontinuation approaches. This survey-based study included pediatric rheumatologists with at least one year of clinical experience in managing cr-FMF. The survey assessed physician characteristics, treatment practices including initiation, tapering, and discontinuation strategies. Data were collected via an online survey platform between September and November 2025. A total of 81 pediatric rheumatologists participated, mostly practicing in Türkiye (92.6%). Most respondents preferred once-daily anakinra at 1-2 mg/kg/day and assessed response within the first month. Among tapering strategies, 90.1% favored interval extension, most commonly every 3 days or weekly. 79.0% considered discontinuation after sustained remission (median 6 months). During tapering-related flares, clinicians preferred interval shortening (43.2%) or dose escalation (37.0%), while 19.8% switched to an alternative biologic. After discontinuation-related relapse, 81.5% restarted anakinra at the previous effective dose. While anakinra initiation and relapse management appear relatively consistent, tapering and discontinuation strategies remain highly variable, underscoring the need for evidence-based guidance.

PubMedNigerian medical journal : journal of the Nigeria Medical Association2026-07-19

Echoes of a Cytokine Storm: HLH-Associated Bi-Ventricular Failure in a Young Woman with Lupus - A Case Report.

Uwakwem Chiedozie Nnabue CN, Clark Samuel S

Haemophagocytic lymphohistiocytosis (HLH) is a rare hyperinflammatory syndrome that can lead to rapid multiorgan failure. Cardiovascular involvement is under-recognised but may manifest as acute, reversible cardiomyopathy, particularly in patients with autoimmune disease. Early identification of cardiac complications is essential to guide timely immunosuppression and supportive therapy. A 33-year-old woman with systemic lupus erythematosus (SLE) was transferred for specialist management of HLH. After initial stabilisation, she developed chest pain and haemodynamic compromise. Transthoracic echocardiography revealed severe bi-ventricular failure (EF 18%) and torrential tricuspid regurgitation. She was readmitted to ICU and managed with levosimendan, glyceryl trinitrate, and milrinone. Immunosuppression was escalated with IV methylprednisolone, IVIG, anakinra, etoposide, and rituximab. Cardiac function improved rapidly, guided by serial echocardiography and biomarker monitoring. She was discharged with normalised EF and good functional recovery on tapering steroids and mycophenolate. This case demonstrates that HLH can cause severe but reversible cardiomyopathy, particularly in patients with autoimmune disease. Early echocardiographic assessment and prompt initiation of immunosuppression alongside cardiovascular support enabled full recovery of cardiac function. Timely, multidisciplinary management is essential to prevent irreversible multiorgan dysfunction in HLH.

PubMedNigerian medical journal : journal of the Nigeria Medical Association2026-07-19

HaemophagocyticLymphohistiocytosis Secondary to Severe Falciparum Malaria: A Case Series from a UK Tertiary Centre.

Nnabue Uwakwem Dr Chiedozie DC, Clark Dr Samuel DS

Haemophagocytic lymphohistiocytosis (HLH) is a rare but often fatal hyperinflammatory syndrome that can be triggered by infections, including Plasmodium falciparum. Although HLH secondary to malaria is documented, it remains under-recognised in clinical practice. We describe two cases of HLH complicating severe falciparum malaria, aiming to highlight diagnostic challenges and therapeutic considerations. This is a retrospective case series of two adult female patients admitted to a tertiary intensive care unit (ICU) in London, UK. Clinical data were extracted from the electronic health record (Epic Hyperspace). HLH was diagnosed using HLH-2004 criteria and the HScore (calculated with MDCalc). Both patients were treated with anti-malarials and HLH-directed immunomodulation, including corticosteroids, IVIG, and anakinra. Both patients fulfilled ≥5 of the HLH-2004 criteria and had elevated ferritin (>21,000 and 48,000 μg/L, respectively) with HScore probabilities of 98-99%. One case was confirmed by bone marrow haemophagocytosis. Both required renal replacement therapy and invasive ventilation. Ferritin and organ function improved following combined immunosuppressive therapy, with complete clinical recovery and discharge by days 31 and 32 of illness. Malaria-associated HLH, though rare, should be suspected in adults with severe P. falciparum infection and extreme hyperferritinaemia. Early recognition and immunomodulatory therapy guided by HScore and HLH-2004 criteria can be lifesaving. Clinicians in endemic regions and among returning travellers should maintain vigilance for HLH in cases of severe malaria unresponsive to standard treatment.

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